RESUMO
Osteogenesis Imperfecta leads to alterations in type 1 collagen fiber, apart from causing bone fracture, blue sclera and other related deformities. As few medical records are available in the field of dentistry regarding these alterations, having a better understanding of this medical disorder and its dental management has become a matter of extreme relevance if one is to provide adequate treatment for patients suffering from this medical condition. This paper reports the case of a 2-year old patient with Osteogenesis Imperfecta who received treatment as part of the Acolher Project PNE run by the Federal Fluminense University in Rio de Janeiro, Brazil. (AU)
Osteogênese Imperfeita leva a alteração na fibra colágena tipo I, ocasiona fraturas ósseas, escleras azuladas e outras deformidades. Essa alteração apresenta poucos registros científicos no ramo da odontologia sendo extremamente importante para as áreas de Pacientes Especiais, Odontopediatria e Odontologia Hospitalar no entendimento dessa desordem e o manejo odontológico. Este estudo relata o caso de uma paciente de 2 anos de idade com Osteogênese Imperfeita atendida no Projeto AcolherPNEUFF.(AU)
